@prefix vh8: <http://data.loterre.fr/ark:/67375/VH8> .
@prefix skos: <http://www.w3.org/2004/02/skos/core#> .

vh8:-RSBS7B77-7
  skos:prefLabel "coagulopathy"@en, "coagulopathie"@fr ;
  a skos:Concept ;
  skos:narrower vh8:-GWPN610V-5 .

vh8:-N32K7HZ8-D
  skos:prefLabel "hereditary disease"@en, "maladie héréditaire"@fr ;
  a skos:Concept ;
  skos:narrower vh8:-GWPN610V-5 .

vh8: a skos:ConceptScheme .
vh8:-GWPN610V-5
  skos:definition "Scott syndrome is a rare congenital bleeding disorder that is due to a defect in a platelet mechanism required for blood coagulation. Normally when a vascular injury occurs, platelets are activated and phosphatidylserine (PS) in the inner leaflet of the platelet membrane is transported to the outer leaflet of the platelet membrane, where it provides a binding site for plasma protein complexes that are involved in the conversion of prothrombin to thrombin, such as factor VIIIa-IXa (tenase) and factor Va-Xa (prothrombinase).In Scott syndrome, the mechanism for translocating PS to the platelet membrane is defective, resulting in impaired thrombin formation. (Wikipedia)"@en ;
  a skos:Concept ;
  skos:inScheme vh8: ;
  skos:broader vh8:-RSBS7B77-7, vh8:-N32K7HZ8-D ;
  skos:prefLabel "syndrome de Scott"@fr, "Scott syndrome"@en ;
  skos:exactMatch <https://www.wikidata.org/wiki/Q7437571>, <https://en.wikipedia.org/wiki/Scott_syndrome> .