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Human Diseases (thesaurus)

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Concept information

disease > genetic disease > hereditary disease > non-bullous ichtyosiform erythroderma
disease > congenital disease > non-bullous ichtyosiform erythroderma
... > disease > skin appendages disease > skin disease > erythroderma > ichtyosiform erythroderma > non-bullous ichtyosiform erythroderma
... > disease > skin appendages disease > skin disease > dyskeratosis > hyperkeratosis > ichthyosis > non-bullous ichtyosiform erythroderma

Terme préférentiel

non-bullous ichtyosiform erythroderma  

Définition

  • Lamellar ichthyosis, also known as ichthyosis lamellaris and nonbullous congenital ichthyosis, is a rare inherited skin disorder, affecting around 1 in 600,000 people. (Wikipedia)

Synonyme(s)

  • lamellar ichtyoses
  • lamellar ichtyosis

Traductions

URI

http://data.loterre.fr/ark:/67375/VH8-W7B3GJ02-T

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