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Human Diseases (thesaurus)

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Concept information

disease > genetic disease > hereditary disease > bullous ichtyosiform erythroderma
... > disease > skin appendages disease > skin disease > dyskeratosis > hyperkeratosis > bullous ichtyosiform erythroderma
... > disease > skin appendages disease > skin disease > dermatosis > bullous dermatosis > bullous ichtyosiform erythroderma

Terme préférentiel

bullous ichtyosiform erythroderma  

Définition

  • Epidermolytic ichthyosis (EI), also known as bullous epidermis ichthyosis (BEI), epidermolytic hyperkeratosis (EHK), bullous congenital ichthyosiform erythroderma (BCIE), bullous ichthyosiform erythroderma or bullous congenital ichthyosiform erythroderma Brocq, is a rare and severe form of ichthyosis this skin disease affects around 1 in 300,000 people. (Wikipedia)

Synonyme(s)

  • epidermolytic hyperkeratosis

Traductions

URI

http://data.loterre.fr/ark:/67375/VH8-C4NHTKSL-L

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