Concept information
Término preferido
Malignant Atrophic Papulosis
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Tipo
-
mesh:Descriptor
Definición
- Variously described as a vasculopathy, endovasculitis, or occlusive arteriopathy, this condition occurs in a benign cutaneous form and a lethal multiorgan systemic variant. It is characterized by a narrowing and occlusion of the lumen of small to medium-sized blood vessels, leading to ischemia and infarction in the involved organ systems. The etiology and pathophysiology are unknown.
Concepto genérico
Etiquetas alternativas
- Degos Disease
- Degos Syndrome
- Degos's Malignant Atrophic Papulosis
- Erythrokeratoderma en cocardes
- Kohlmeier-Degos Disease
- Papulosis, Malignant Atrophic
En otras lenguas
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francés
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Érythrokératodermie en cocardes
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Maladie de Degos
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Maladie de Köhlmeier-Degos
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Syndrome cutanéo-intestinal mortel
URI
http://data.loterre.fr/ark:/67375/JVR-DCRPMBM7-P
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